Abstract

Left ventricular hypoplasia is a severe congenital heart disease with a currently reserved prognosis, even for patients who can be treated in the newborn period, either because they have been diagnosed early at birth or because the diagnosis was made in the fetal period. The latter is important because it allows the medical team to be prepared and to offer the patient the best management conditions in the neonatal period and a surgical treatment appropriate to their pathology and in the best situation in a tertiary level cardiac surgical center. We present a case with an antenatal diagnosis where all the stages were carried out to provide an adequate treatment, but due to the complexity of the case the parents opted for compassionate treatment.

Keywords

hypoplastic left heart syndrome, atretic stenosis, protein-losing enteropathy, cardiac malformation